Generalized Lymphangiomatosis: Rare Hepatic and Pulmonary Presentation - Abstract
Lymphangiomas are rare benign neoplasms believed to be result of abnormal development of lymphatic system. They grow very slowly usually localized to one organ, but occasionally involve several organs in one part of the body. Reports of single organ involvement have been published relating to nearly all organs of the body except CNS with certain predilection tocervicothoracic region. Lymphangiomatosis or multifocal/ diffuse lymphangiomas presented during childhood mainly in the head and neck region; less than 5% are intra-abdominal. In one large series, lymphangioma of head and neck accounted for nearly 50% of cases in children, while 10% of cases had visceral disease including thorax. We report 4-year-old child with lymphangiomatosis having cannon ball opacities on chest radiograph and simultaneous pulmonary and hepatic involvement which has never been reported and is unusual presentation.