Umbilical endometriosis, also known as Villar’s nodule, is defined as an ectopic localization of functional endometrium at the umbilicus. It is rare, with an incidence ranging from 0.5 to 1.2% of all patients with endometriosis. Clinically, it presents as a solitary, solid, well-defined nodule, colored in red, blue, or black, occasionally accompanied by bleeding and cyclic dysmenorrhea. Its treatment can be medical or surgical, involving analgesics and hormonal suppression using Gonadotropin-Releasing Hormone (GnRH) analogs, hormonal contraceptives, danazol, or progesterone. Surgical treatment involves complete resection of the umbilical lesion. This disease often poses the challenge of differential diagnosis with Sister Mary Joseph’s nodule. It is also a cause of couple infertility. Despite the clinically recognized association between endometriosis and infertility, the mechanisms involved in infertility associated with endometriosis are not fully understood. Umbilical endometriosis is a rare localization of the disease. It is in this context that we report a case. He was a 34-year-old homemaker who presented to the clinic with umbilical pain persisting for 2 years, followed by a painful swelling at the umbilicus 8 months later6-. She reported pain associated with menstruation for the past 4 months, with bright red bloody discharge occurring with each menstrual cycle, subsiding a few days after the cycle. She had been taking analgesics routinely for the pain, but the persistence of bleeding with each cycle prompted her to seek medical attention. The patient had a history of ectopic pregnancy 10 years ago and had a history of 3 pregnancies, 1 live birth, and 2 spontaneous miscarriages. Primary umbilical endometriosis, also known as Villar’s nodule, is a rare but often confusing pathology with other tumorous dermatoses of the umbilicus. Its management always involves a multidisciplinary approach.