Abrikossoff’s granular cell tumour is rare, developing between the ages of 20 and 60, with a female predominance, ubiquitous location and a predilection for the mucosa of the ENT and oral cavity. We report here the case of an Abrikossoff’s tumor localized on the inner side of the right thigh. Usually benign and single but can be malignant and multifocal. The pathogenesis has long been debated but recent studies favour a Schwannian origin confirmed by immunohistochemical study. The treatment of granular cell tumours is surgical, allowing a diagnosis of certainty by anatomical-pathological examination of the excisional piece. The outcome is often favourable if complete surgical resection is performed.