Chordomas are rare malignant neoplasms derived from incomplete regression of notochordal tissue along the cranio-coccygeal axis. We report a case of retropharyngeal chordoma presenting with dysphagia and operated on by trans oral approach associated a post-operative radiotherapy. Chordomas must to be evocated in retrophayngeal tumors required a good checking (imaging, cytology) and conformed by immunohistological exam. The prognosis is poor.