Introduction : Sialoblastoma is a rare, congenital malignant epithelial tumor of the salivary glands. It is located mainly in the parotid and maxillary glands. Its location in the sublingual gland is exceptional.
Summary of the clinical case : We report the case of a 10-month-old infant, with no pathological history, who consulted for a congenital mass under left mandibular, gradually increasing in volume.
The examination found a left submandibular mass of about 10 centimeters long axis, firm, mobile compared to the 2 planes, painless with a healthy skin.
The cervical CT showed a left mandibular mass, tissue, with regular contours; without lymphadenopathy.
The patient had a complete excision of the mass under general anesthesia. Intraoperatively, we found a mass of cerebral aspect extending forward and inward of the left maxillary gland which was normal in appearance. The postoperative course was simple. Anatomopathological examination of the operative specimen concluded with sialoblastoma.
Conclusion : Topographical diagnosis of the sialoblastoma of sublingual gland is possible in peroperatory. There is no consensus on the  which is essentially surgical by complete exeresis.